{"id":5947,"date":"2021-06-25T12:15:28","date_gmt":"2021-06-25T12:15:28","guid":{"rendered":"https:\/\/turkeyistanbulmedical.com\/?p=5947"},"modified":"2022-01-19T13:24:29","modified_gmt":"2022-01-19T13:24:29","slug":"kartagener-sendromu","status":"publish","type":"post","link":"https:\/\/turkeyistanbulmedical.com\/tr\/kartagener-sendromu\/","title":{"rendered":"Kartagener Sendromu"},"content":{"rendered":"<h2><strong>Kartagener Sendromu<\/strong><\/h2>\n<p><strong>Kartagener Sendromu,<\/strong>\u00a0bron\u015fektezi, tekrarlayan sin\u00fczit ve sol taraftaki organlar\u0131n sa\u011f tarafta olmas\u0131 anlam\u0131na gelen situs inversus birlikteli\u011fi anlam\u0131na gelen bir durumdur.<\/p>\n<p>En \u00f6nemli belirtisi kalbin sol tarafta olmas\u0131 gerekirken sa\u011f tarafta olmas\u0131d\u0131r. Kalbi sa\u011fda olan bir ki\u015fide akci\u011ferde harabiyet nedeniyle bron\u015fektezi olu\u015fur. Ayr\u0131ca tekrarlayan sin\u00fczit de varsa Kartagener sendromu olmas\u0131 ihtimali \u00e7ok y\u00fcksektir.<\/p>\n<h3><strong>Kartagener Sendromu Genetik mi?<\/strong><\/h3>\n<p>Bu hastal\u0131k otozamal resesif kal\u0131t\u0131m g\u00f6sterir. Yani Kartagener sendromlu \u00e7ocu\u011fu olan bir ailenin ikinci \u00e7ocu\u011funun Kartagener sendromlu olma ihtimali %25\u2019tir.<\/p>\n<h4><strong>Kartagener Sendromu G\u00f6r\u00fclme S\u0131kl\u0131\u011f\u0131 nedir?<\/strong><\/h4>\n<p>Her do\u011fan 30 bin \u00e7ocuktan biri bu hastal\u0131kla do\u011far.<\/p>\n<h4><strong>Kartagener Sendromunda Tan\u0131<\/strong><\/h4>\n<p>Kartagener sendromlu hastalar\u0131n yakla\u015f\u0131k yar\u0131s\u0131nda 3 bulgu varken yar\u0131s\u0131nda olmayabilir. Bu bulgular;<\/p>\n<p><img class=\"alignnone size-full wp-image-5943\" src=\"https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome.jpg\" alt=\"kartagener syndrome\" width=\"2400\" height=\"1020\" srcset=\"https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome.jpg 2400w, https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome-300x128.jpg 300w, https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome-1024x435.jpg 1024w, https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome-768x326.jpg 768w, https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome-1536x653.jpg 1536w, https:\/\/turkeyistanbulmedical.com\/wp-content\/uploads\/2021\/06\/clinic-triad-kartagener-syndrome-2048x870.jpg 2048w\" sizes=\"(max-width: 2400px) 100vw, 2400px\" \/><\/p>\n<ul>\n<li><strong>Situs inversus<\/strong>\u00a0(Solda olmas\u0131 gereken organlar\u0131n sa\u011fda olmas\u0131); Organlar\u0131n yerleri de\u011fi\u015fik olan \u00e7ocuklar\u0131n yakla\u015f\u0131n %15-20\u2019sinde <a href=\"https:\/\/turkeyistanbulmedical.com\/tr\/\">Kartagener sendromu<\/a> vard\u0131r. K\u0131saca organlar\u0131n yerleri de\u011fi\u015fik olan her \u00e7ocukta Kartagener geli\u015fmeyebilir.<\/li>\n<li><b>Sin\u00fczit;<\/b> Silia denilen salg\u0131lar\u0131n temizlenmesini sa\u011flayan t\u00fcylerin hareketinin bozulmas\u0131 sonucu s\u0131k tekrarlayan sin\u00fczit de birliktedir<\/li>\n<li><strong>Bron\u015fektazi;<\/strong>\u00a0Silia bozuldu\u011funda mikroplar akci\u011ferlerden temizlenemez ve mikroplar akci\u011ferde yerle\u015fir. Enfeksiyonlar tekrar ederek bron\u015flar zarar g\u00f6r\u00fcr ve bron\u015fektazi geli\u015fir.<\/li>\n<\/ul>\n<h4><strong>\u00a0Belirtileri Nelerdir?<\/strong><\/h4>\n<ul>\n<li>Kalbin sa\u011f tarafta olmas\u0131<\/li>\n<li>Akci\u011ferlerde bron\u015fektazi nedeniyle s\u0131k s\u0131k \u00f6ks\u00fcr\u00fck, balgam, ate\u015f olmas\u0131<\/li>\n<li>S\u0131k s\u0131k sin\u00fczitin g\u00f6r\u00fclmesi<\/li>\n<li>S\u0131k balgaml\u0131 \u00f6ks\u00fcr\u00fck<\/li>\n<li>Erkeklerde infertilite<\/li>\n<\/ul>\n<h4><strong>Genetik \u00d6zellikleri Nelerdir?<\/strong><\/h4>\n<ul>\n<li>Silia bozuklu\u011fu nedeniyle gen mutasyonlar\u0131 ger\u00e7ekle\u015fir ve yakla\u015f\u0131k 30\u2019a yak\u0131n genetik mutasyon tespit edilmi\u015ftir.<\/li>\n<li>Bu nedenle Kartagener sendromlu \u00e7ocu\u011fu olanlar ikinci \u00e7ocuk d\u00fc\u015f\u00fcnd\u00fc\u011f\u00fc zaman genetik tan\u0131 yap\u0131lmas\u0131 \u00f6nemlidir.<\/li>\n<li>Do\u011fum \u00f6ncesi tan\u0131 i\u00e7in bu \u00e7ok \u00f6nemlidir. Gen mutasyonlar\u0131n\u0131n %65 belirlenebilir.<\/li>\n<\/ul>\n<h4><strong>Kartagener<\/strong> <strong>\u00a0Sendromu Tedavisi<\/strong><\/h4>\n<p>Bron\u015fektazisi olan \u00e7ocuklar\u0131n akci\u011ferlerinde a\u015f\u0131r\u0131 balgam nedeniyle balgam birikmesi s\u00f6z konusudur. Bunu engellemek amac\u0131yla postural direnaj yap\u0131lmal\u0131d\u0131r. Bunun i\u00e7in g\u00f6\u011f\u00fcs fizyoterapisi yap\u0131l\u0131r ve balgam k\u00fclt\u00fcr\u00fcnde mikrop \u00fcreyenlere antibiyotik verilmelidir.<\/p>\n<h4><strong>Yap\u0131lmas\u0131 Gereken A\u015f\u0131lar<\/strong><\/h4>\n<p>Kartagener <strong>\u00a0<\/strong>sendromlu \u00e7ocuklara her y\u0131l\u0131n eyl\u00fcl veya ekim ay\u0131nda grip a\u015f\u0131s\u0131 yap\u0131lmal\u0131d\u0131r. Ayr\u0131ca pn\u00f6mokok a\u015f\u0131s\u0131 da yap\u0131lm\u0131\u015f olmas\u0131 gerekir.<\/p>\n<h4><strong>Balgamda s\u0131k \u00fcreyen mikroplar<\/strong><\/h4>\n<ul>\n<li>H.influenza (%58)<\/li>\n<li>S. pneumoniae (%21)<\/li>\n<li>S. aureus (%19)<\/li>\n<li>P. aeruginosa (%14)<\/li>\n<li>E.coli (%10)<\/li>\n<\/ul>\n<h4><strong>Kartagener<\/strong> <strong>\u00a0Sendromunda uygulanan Cerrahi<\/strong><\/h4>\n<p>S\u0131k kulak iltihab\u0131 olanlarda kulak t\u00fcp\u00fc tak\u0131labilir. Bron\u015fektazi ciddi seyretmesi durumunda ve cerrahiye uygun olan durumlarda hasarl\u0131 b\u00f6lge cerrahi olarak \u00e7\u0131kar\u0131labilir.<\/p>\n<h4><strong>Kartagener<\/strong> <strong>\u00a0Sendromunu i\u00e7in Hangi Doktorlara Ba\u015fvurulmal\u0131d\u0131r?<\/strong><\/h4>\n<p>Kartagener sendromu olan \u00e7ocuklar \u00c7ocuk G\u00f6\u011f\u00fcs Hastal\u0131klar\u0131 uzmanlar\u0131 taraf\u0131ndan takip edilir. Akci\u011ferler yak\u0131ndan izlenmeli ve solunum fonksiyonlar\u0131 belirli aral\u0131klarla takip edilmelidir. Genetik tan\u0131 i\u00e7in de genetik b\u00f6l\u00fcm\u00fcnden takip yap\u0131l\u0131r.<\/p>\n<p><strong>Kaynak :<\/strong> <a href=\"https:\/\/www.invitra.com\/en\/kartagener-syndrome\/\" target=\"_blank\" rel=\"noopener\">https:\/\/www.invitra.com\/en\/kartagener-syndrome\/<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Kartagener Sendromu Kartagener Sendromu,\u00a0bron\u015fektezi, tekrarlayan sin\u00fczit ve sol taraftaki organlar\u0131n sa\u011f tarafta olmas\u0131 anlam\u0131na gelen situs inversus birlikteli\u011fi anlam\u0131na gelen bir durumdur. En \u00f6nemli belirtisi kalbin sol tarafta olmas\u0131 gerekirken sa\u011f tarafta olmas\u0131d\u0131r. Kalbi sa\u011fda olan bir ki\u015fide akci\u011ferde harabiyet nedeniyle bron\u015fektezi olu\u015fur. Ayr\u0131ca tekrarlayan sin\u00fczit de varsa Kartagener sendromu olmas\u0131 ihtimali \u00e7ok y\u00fcksektir. Kartagener [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":5938,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":[],"categories":[1215],"tags":[1282],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v17.5 (Yoast SEO v18.4.1) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Kartagener Sendromu - Turkey Istanbul Medical<\/title>\n<meta name=\"description\" content=\"Kartagener Sendromu,\u00a0bron\u015fektezi, tekrarlayan sin\u00fczit ve sol taraftaki organlar\u0131n sa\u011f tarafta olmas\u0131 anlam\u0131na gelen situs inversus birlikteli\u011fi anlam\u0131na\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/turkeyistanbulmedical.com\/tr\/kartagener-sendromu\/\" \/>\n<meta property=\"og:locale\" content=\"tr_TR\" \/>\n<meta property=\"og:type\" content=\"article\" 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